[Successful treatment with prednisone in a critical ill newborn with symptomatic multifocal infantile hepatic hemangioendothelioma].

نویسندگان

  • Miurkis Endis Miranda
  • Ramón Villamil Martínez
  • Pastor Alexander Thomas Olivares
  • Juan Jose Trujillo Gálvez
چکیده

Infantile hepatic hemangioendothelioma is the most common vascular tumor of the liver in infancy. The diagnosis can be enunciated without histological defnition, if the clinical, analytical and images fndings are very suggestive; particularly in children less than six months old, because the biopsy is not exempt of complications. We report a female patient, four days old and 3500 g, who developed a hypovolemic shock as a complication of the biopsy from a multifocal infantile hepatic hemangioendothelioma. She developed clinical manifestations of cardiac failure and thrombocytopenia. Because of the critical clinical status we choose the medical treatment with prednisone which was administered for fve month and complete remission of the tumor was obtained. We highlight the Doppler ultrasonography as a safe and no invasive diagnosis method. Management of this disease is commented as well.

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عنوان ژورنال:
  • Archivos argentinos de pediatria

دوره 111 5  شماره 

صفحات  -

تاریخ انتشار 2013